Case Report
Copyright ©The Author(s) 2017. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Orthop. Sep 18, 2017; 8(9): 735-740
Published online Sep 18, 2017. doi: 10.5312/wjo.v8.i9.735
Using humeral nail for surgical reconstruction of femur in adolescents with osteogenesis imperfecta
Paphon Sa-ngasoongsong, Tanyawat Saisongcroh, Chanika Angsanuntsukh, Patarawan Woratanarat, Pornchai Mulpruek
Paphon Sa-ngasoongsong, Tanyawat Saisongcroh, Chanika Angsanuntsukh, Patarawan Woratanarat, Pornchai Mulpruek, Department of Orthopedics, Faculty of Medicine Ramathibodi Hospital, Mahidol University, Bangkok 10400, Thailand
Author contributions: Sa-ngasoongsong P and Mulpruek P performed all operations together; Sa-ngasoongsong P drafted manuscript; Saisongcroh T collected the patients’ clinical data and drafted the manuscript; Angsanuntsukh C and Woratanarat P provided material and technical support; Mulpruek P designed the study and revised manuscript for important intellectual content; all authors have read and approved the final version to be published.
Institutional review board statement: The study was reviewed and approved by the Ethical Clearance Committee on Human Rights to Research Including Human Subjects, Faculty of Medicine Ramathibodi Hospital, Mahidol University (Protocol ID 02-58-67).
Informed consent statement: According to the ethical approval, there was no need for informed consent from individual patients in retrospective study (all data were retrieved from medical records).
Conflict-of-interest statement: All of the authors declare that they have no conflict of interest.
Open-Access: This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
Correspondence to: Pornchai Mulpruek, MD, Clinical Professor, Department of Orthopedics, Faculty of Medicine Ramathibodi Hospital, Mahidol University, 270, Rama VI Road, Ratchathewi, Bangkok 10400, Thailand. pornchai.mul@mahidol.ac.th
Telephone: +66-2-2011589 Fax: +66-2-2011599
Received: January 27, 2017
Peer-review started: February 12, 2017
First decision: June 12, 2017
Revised: June 16, 2017
Accepted: July 21, 2017
Article in press: July 22, 2017
Published online: September 18, 2017
Abstract

Osteogenesis imperfecta (OI) is a rare inherited connective tissue disorder caused by mutation of collagen which results in a wide spectrum of clinical manifestations including long bone fragility fractures and deformities. While the treatment for these fractures was recommended as using intramedullary fixation for minimizing stress concentration, the selection of the best implant in the adolescent OI patients for the surgical reconstruction of femur was still problematic, due to anatomy distortion and implant availability. We are reporting the surgical modification by using a humeral nail for femoral fixation in three adolescent OI patients with favorable outcomes.

Keywords: Osteogenesis imperfecta, Adolescent, Humeral nail, Femoral fracture, Femoral bowing deformity

Core tip: This case report presented the satisfactory clinical outcome of the adolescent osteogenesis imperfecta patients suffering from femoral fracture or bowing deformity which had been treated with the modification of humeral nail as intramedullary implant.