Published online Dec 14, 2014. doi: 10.3748/wjg.v20.i46.17674
Revised: June 8, 2014
Accepted: July 11, 2014
Published online: December 14, 2014
Type 1 autoimmune pancreatitis (AIP) or chronic sclerosing sialadenitis (Küttner’s tumour) is an uncommon disorder that has recently been confirmed as an IgG4-related disease. Here, we describe a rare case of a 53-year-old male patient who primarily presented with pancreatic body mass, left neck mass and several lumps in his lower lip mimicking pancreatic cancer (PC) and neck metastasis. The patient underwent pancreatic body mass and labial gland lumps resection as well as an ultrasound-guided biopsy of the left neck mass. He was diagnosed with IgG4-related focal type of AIP (f-AIP) and Küttner’s tumour by immunohistochemistry. The patient responded well to corticosteroid therapy and remains healthy with no signs of recurrence at one year follow-up. The differentiation of f-AIP from PC is very important to avoid unnecessary pancreatic resection.
Core tip: We report a rare case of 53-year-old male patient who suffered from IgG4-related focal type of autoimmune pancreatitis (f-AIP) accompanied with Küttner’s tumour originally suspected of being pancreatic cancer with neck metastasis. The patient responded well to corticosteroid therapy but he had undergone an unnecessary pancreatic body mass resection one year ago prior to admission. Therefore, we suggest that AIP should always be considered in case of a focal pancreatic mass.