Published online Feb 16, 2017. doi: 10.12998/wjcc.v5.i2.35
Peer-review started: July 3, 2016
First decision: September 5, 2016
Revised: November 19, 2016
Accepted: December 27, 2016
Article in press: December 28, 2016
Published online: February 16, 2017
Core tip: Kikuchi-Fujimoto disease (KFD), or histiocytic necrotizing lymphadenitis, is an uncommon condition, typically characterized by lymphadenopathy and fevers. KFD is an extremely rare disease. With this case we wish to highlight that KFD carries a risk of mortality in the setting of acute, aggressive disease, which is in contrast to the benign, self-limiting condition that has been classically documented in literature. The patient emphasizes the importance of recognizing this as we present the fourth case of disseminated intravascular coagulopathy as a cause of fatality in these patients.