Case Report
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World J Radiol. Jul 28, 2014; 6(7): 507-510
Published online Jul 28, 2014. doi: 10.4329/wjr.v6.i7.507
Bilateral squamosal suture synostosis: A rare form of isolated craniosynostosis in Crouzon syndrome
Yasmeen K Tandon, Michael Rubin, Mohamed Kahlifa, Gaby Doumit, Lena Naffaa
Yasmeen K Tandon, Department of Radiology, Case Western Reserve University-Metro Health Medical Center, Cleveland, OH 44109, United States
Michael Rubin, Lena Naffaa, Department of Radiology, Akron Children’s Hospital, One Perkins Square, Akron, OH 44308, United States
Mohamed Kahlifa, Department of Medical Genetics, Akron Children’s Hospital, One Perkins Square, Akron, OH 44308, United States
Gaby Doumit, Department of Plastic Surgery, Cleveland Clinic, Cleveland, OH 44195, United States
Author contributions: Tandon YK, Rubin M, Kahlifa M, Doumit G and Naffaa L contributed equally to this work; Tandon YK, Naffaa L, Rubin M and Doumit G interpreted images in this study; Tandon YK, Rubin M, Kahlifa, Doumit G and Naffaa L and wrote the paper; Tandon YK, Rubin M, Kahlifa, Doumit G and Naffaa L gave final approval of the version to be published.
Correspondence to: Yasmeen K Tandon, MD, Department of Radiology, Case Western Reserve University-Metro Health Medical Center, 2500 Metro Health Dr, Cleveland, OH 44109, United States. ytandon@neomed.edu
Telephone: +1-216-7784016 Fax: +1- 216-7784375
Received: April 5, 2014
Revised: June 1, 2014
Accepted: June 14, 2014
Published online: July 28, 2014
Processing time: 116 Days and 22.7 Hours
Abstract

Craniosynostosis is a pathologic condition which is characterized by the premature fusion of cranial sutures. It may occur alone or in association with other anomalies making up various syndromes. Crouzon syndrome is the most common craniosynostosis syndrome. Bicoronal sutures fusion is most commonly involved in Crouzon syndrome. There have only been a handful of cases of squamosal suture synostosis described in the surgery literature with the few ones described in Crouzon syndrome associated with other types of craniosynostosis. To the best of our knowledge, we are presenting the first case of isolated bilateral squamosal suture synostosis in a patient with Crouzon syndrome in a radiology journal with emphasis on its radiological appearance.

Keywords: Squamosal; Suture; Craniosynostosis; Crouzon; Syndrome

Core tip: We report the unique case of isolated bilateral squamosal suture synostosis in a 13-mo old patient with Crouzon syndrome. Although bicoronal sutures are most commonly involved in patients with Crouzon syndrome, it is important to be familiar with this rare entity of craniosynostosis in order to prevent misdiagnosis or delayed surgical treatment.