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World J Gastroenterol. May 7, 2014; 20(17): 5157-5164
Published online May 7, 2014. doi: 10.3748/wjg.v20.i17.5157
Published online May 7, 2014. doi: 10.3748/wjg.v20.i17.5157
Clinical and computed tomography features of adult abdominopelvic desmoplastic small round cell tumor
Xun-Ze Shen, Department of Radiology, Shaoxing People’s Hospital, Shaoxing Hospital of Zhejiang University, Shaoxing 312000, Zhejiang Province, China
Jian-Guo Zhao, Department of Radiotherapy, Shaoxing People’s Hospital, Shaoxing Hospital of Zhejiang University, Shaoxing 312000, Zhejiang Province, China
Jian-Jun Wu, Department of Radiology, Second Affiliated Hospital of Medical School, Zhejiang University, Hangzhou 312009, Zhejiang Province, China
Fang Liu, Department of Pathology, Shaoxing People’s Hospital, Shaoxing Hospital of Zhejiang University, Shaoxing 312000, Zhejiang Province, China
Author contributions: Shen XZ designed the research and wrote the paper; Zhao JG and Wu JJ revised the paper; Liu F analyzed the pathological figures.
Correspondence to: Xun-Ze Shen, MD, Associate Chief Physician, Department of Radiology, Shaoxing People’s Hospital, Shaoxing Hospital of Zhejiang University, Yuecheng Downtown, Shaoxing 312000, Zhejiang Province, China. shenxunze@163.com
Telephone: +86-575-88228548 Fax: +86-575-88228899
Received: October 7, 2013
Revised: December 22, 2013
Accepted: January 20, 2014
Published online: May 7, 2014
Revised: December 22, 2013
Accepted: January 20, 2014
Published online: May 7, 2014
Core Tip
Core tip: Desmoplastic small round cell tumor (DSRCT) is a rare abdominopelvic malignancy with multicentric growth. The third decade may be a peak period of incidence, and the disease can also occur in older people. Computed tomography can display characteristic features that are helpful in diagnosis of DSRCT. Prognosis and overall survival rates are generally poor. Early discovery and complete resection, coupled with postoperative adjuvant chemotherapy, are important for prognosis of DSRCT. Whole abdominopelvic rather than locoregional radiotherapy is more effective for unresectable DSRCT.