Case Report
Copyright ©2009 The WJG Press and Baishideng. All rights reserved.
World J Gastroenterol. Sep 7, 2009; 15(33): 4212-4214
Published online Sep 7, 2009. doi: 10.3748/wjg.15.4212
Retroperitoneal desmoplastic small round cell tumor: Pediatric patient treated with multimodal therapy
Yong Seok Kim, Seong Jae Cha, Yoo Shin Choi, Beom Gyu Kim, Sung Jun Park, In Taik Chang
Yong Seok Kim, Seong Jae Cha, Yoo Shin Choi, Beom Gyu Kim, Sung Jun Park, In Taik Chang, Department of Surgery, College of Medicine, Chung-Ang University, Seoul 156-755, South Korea
Author contributions: Kim YS and Choi YS designed and performed the research; Cha SJ analyzed the data and images; Kim BG, Park SJ and Chang IT provided their advices.
Correspondence to: Yoo Shin Choi, MD, Department of Surgery, College of Medicine, Chung-Ang University, 224-1, Heuk Seok-Dong, Dongjak-Ku, Seoul 156-755, South Korea. ushinchoi@hotmail.com
Telephone: +82-2-62991545 Fax: +82-2-8247869
Received: May 26, 2009
Revised: July 29, 2009
Accepted: August 5, 2009
Published online: September 7, 2009
Abstract

A desmoplastic small round cell tumor (DSRCT) is a rare, aggressive mesenchymal neoplasm. Although a DSRCT can develop at various sites, the intra-abdominal site is the most common location. These tumors are found most commonly among young adolescents and the prognosis is extremely poor. Multimodal treatment with surgery, chemotherapy and radiotherapy is very important for these rare cases, and this treatment can improve patient survival. In this report, we describe the case of an 8-year-old boy diagnosed with DSRCT located in the retroperitoneal space. The patient has undergone surgical resection and adjuvant chemoradiation therapy, and is currently alive without disease recurrence.

Keywords: Retroperitoneum, Desmoplastic small round cell tumor, Multimodal therapy