Congenital pulmonary airway malformation of a congenital lung disease with a potential hybrid lesion: A case report

Table 1 Features of congenital pulmonary airway malformation as per Stocker classification

Types	Site of origin	Morphological features	Prognosis
Type 0	Trachea/bronchi	Bronchial type airways with cartilage, smooth muscles, and glands separated by mesenchyme	Incompatible with life
Type 1	Bronchi	Multiloculated cysts, lined by pseudo-stratified columnar epithelium and located within one lobe	Excellent prognosis following resection. Rarely undergoes malignant transformation
Type 2	Bronchiolar region	Multiple small cysts with no mass effect	Good prognosis with no malignant potential
Type 3	Bronchiolar regions	Involves and expands an entire lobe compressing the other lobes, maybe solid or cystic. Absent pulmonary arteries within the lesion	Good prognosis with no malignant potential
Type 4	Acinar structures of the lung	Peripheral thin-walled multiloculated cysts, lined by alveolar type 1 or type 2 cells	Strong association with type 1 pleuro-pulmonary blastomas[2,3]