Published online Feb 8, 2018. doi: 10.5409/wjcp.v7.i1.27
Peer-review started: October 29, 2017
First decision: December 8, 2017
Revised: December 13, 2017
Accepted: December 28, 2017
Article in press: December 28, 2017
Published online: February 8, 2018
Core tip: The diagnosis of Kawasaki disease poses several challenges for the treating pediatricians as it is based on a set of criteria that are entirely clinical. To further complicate matters, several children present with incomplete and atypical forms of the disease. It is known that children with incomplete and atypical Kawasaki disease do not have milder form of the disease, rather the rate of coronary and non-coronary complications may even be higher in these subgroups as the diagnosis often gets delayed. While intravenous immunoglobulin remains the cornerstone of management, several children require additional form of therapy thereby further challenging the clinical skills and judgment of the pediatricians.