Case Report
Copyright ©The Author(s) 2022. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Cardiol. Jan 26, 2022; 14(1): 54-63
Published online Jan 26, 2022. doi: 10.4330/wjc.v14.i1.54
Anesthetic management of a child with Cornelia de Lange Syndrome undergoing open heart surgery: A case report
Oguzhan Arun, Bahar Oc, Esma Nur Metin, Ahmet Sert, Resul Yilmaz, Mehmet Oc
Oguzhan Arun, Bahar Oc, Esma Nur Metin, Department of Anesthesiology and Reanimation, Selcuk University Faculty of Medicine, Konya 42130, Turkey
Ahmet Sert, Department of Pediatric Cardiology, Selcuk University Faculty of Medicine, Konya 42130, Turkey
Resul Yilmaz, Pediatric Intensive Care, Selcuk University Faculty of Medicine, Konya 42130, Turkey
Mehmet Oc, Department of Cardiovascular Surgery, Selcuk University Faculty of Medicine, Konya 42130, Turkey
Author contributions: All authors equally contributed to the preparation of the manuscript; Arun O analyzed the data and wrote the manuscript; all authors have read and approved the final manuscript.
Informed consent statement: Written informed consent was obtained from the father of the patient for publication of this report and accompanying images.
Conflict-of-interest statement: The authors certify that there is no conflict of interest with any financial organization regarding the material discussed in the manuscript.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Oguzhan Arun, MD, Professor, Department of Anesthesiology and Reanimation, Selcuk University Faculty of Medicine, Alaaddin Keykubat Kampus, Konya 42130, Turkey. oguzarun@selcuk.edu.tr
Received: April 2, 2021
Peer-review started: April 2, 2021
First decision: June 25, 2021
Revised: July 14, 2021
Accepted: December 21, 2021
Article in press: December 21, 2021
Published online: January 26, 2022
Core Tip

Core tip: Cornelia de Lange Syndrome (CdLS) is a congenital multisystemic genetic disorder with multiple congenital abnormalities. The expected lifespan of children with CdLS has been prolonged in parallel with the advances in medicine in recent years. Patients with CdLS undergo cardiac surgery more frequently. In any patients with multiple medical challenges, anesthesiologists, cardiovascular surgeons and pediatricians may face unexpectedly unusual perioperative courses with additional difficulties when undergoing congenital open-heart surgery. The case presented here demonstrates an example of a challenging perioperative management period of a child with multisystemic congenital disease undergoing multiple high-risk surgeries.