Published online Sep 27, 2019. doi: 10.4240/wjgs.v11.i9.358
Peer-review started: May 9, 2019
First decision: June 12, 2019
Revised: July 8, 2019
Accepted: August 7, 2019
Article in press: August 7, 2019
Published online: September 27, 2019
Core tip: Pseudomyxoma peritonei is an orphan disease that explains the misunderstanding around this nosologic entity. There is still controversy over its definition and classification. Cystadenocarcinoma of the ovary has been repeatedly and wrongly stated as an important etiology of pseudomyxoma. The aim of the present review is to provide clarifications on misconceptions surrounding PMP and to explain the historical sources from which such misconceptions have been drawn.