Beltrán &DG, Martínez AV, Manrique MDCP, Rodríguez JS, Febres EL, Peña SR. Superior mesenteric artery syndrome in a patient with Charcot Marie Tooth disease. World J Gastrointest Surg 2011; 3(12): 197-200 [PMID: 22224174 DOI: 10.4240/wjgs.v3.i12.197]
Corresponding Author of This Article
Óscar Dario Gómez Beltrán, MD, Department of General Surgery, Reina Sofia Teaching Hospital, Córdoba 14004, Spain. medicinaunosc@hotmail.com
Article-Type of This Article
Case Report
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World J Gastrointest Surg. Dec 27, 2011; 3(12): 197-200 Published online Dec 27, 2011. doi: 10.4240/wjgs.v3.i12.197
Superior mesenteric artery syndrome in a patient with Charcot Marie Tooth disease
Óscar Dario Gómez Beltrán, Amparo Valverde Martínez, María del Carmen Pérez Manrique, Joaquín Sánchez Rodríguez, Enrique Lizárraga Febres, Sebastián Rufián Peña
Óscar Dario Gómez Beltrán, Amparo Valverde Martínez, María del Carmen Pérez Manrique, Joaquín Sánchez Rodríguez, Enrique Lizárraga Febres, Sebastián Rufián Peña, Department of General Surgery, Reina Sofía Teaching Hospital, Córdoba 14004, Spain
Author contributions: Gómez Beltrán ÓD and Valverde Martínez A contributed equally to this study; Sánchez Rodríguez J, Pérez Manrique MC, Gómez Beltrán ÓD and Valverde Martínez A designed the study; Valverde Martínez A and Gómez Beltrán ÓD performed the research and wrote the paper; Rufián Peña S, Sánchez Rodríguez J and Lizarraga Febres E revised the work critically and approved the version to be published.
Correspondence to: Óscar Dario Gómez Beltrán, MD, Department of General Surgery, Reina Sofia Teaching Hospital, Córdoba 14004, Spain. medicinaunosc@hotmail.com
Telephone: +34-957-735045 Fax: +34-957-010000
Received: October 25, 2010 Revised: November 3, 2011 Accepted: November 10, 2011 Published online: December 27, 2011
Abstract
The extrinsic compression of the third part of the duodenum as it passes through the aorto-mesenteric angle is known as the superior mesenteric artery syndrome (SMAS). This syndrome is a rare mechanical cause of upper intestinal obstruction, with a reported incidence of between 0.2% and 0.78%. Clinical manifestations of SMAS may be chronic or acute; chronic symptoms include intermittent gastric pain, fullness and occasional episodes of postprandial vomiting, while acute symptoms include incoercible vomiting, oral intolerance, mainly epigastric abdominal distension and abdominal pain. Surgery is recommended only when initial conservative treatment fails. Here, we report what appears to be the third published case of SMAS associated with hereditary motor and sensory neuropathy or Charcot Marie Tooth disease.
