Published online Dec 15, 2016. doi: 10.4251/wjgo.v8.i12.835
Peer-review started: May 3, 2016
First decision: July 5, 2016
Revised: August 25, 2016
Accepted: October 22, 2016
Article in press: October 24, 2016
Published online: December 15, 2016
Rhabdomyomatous well-differentiated esophageal liposarcomas are extremely rare. As of August 2016, only one other such case has been reported in the English-language medical literature. Liposarcomas in general are one of the most common soft tissue neoplasms in adults, but the incidence of primary esophageal liposarcomas is exceptionally low. There have been only 42 reported cases of primary liposarcoma of the esophagus worldwide thus far. These malignancies are harbored within giant fibrovascular polyps, which slowly grow within the esophageal lumen causing obstructing symptoms. We hereby present the case of a 68-year-old male patient who came in with a 2-mo history of worsening intermittent dysphagia, persistent cough, and postprandial retrosternal pain. After an esophagogastroduodenoscopy, a computed tomographic scan, and a diagnostic endoscopy, complete endoscopic resection was performed of the 13 cm × 6 cm × 2.6 cm fibrovascular polyp. A literature review was done and results are presented herein.
Core tip: This is only the second case of a rhabdomyomatous well-differentiated esophageal liposarcoma to be reported in the literature. Both cases clinically presented as standard esophageal liposarcomas housed in a giant fibrovascular polyp until histological examination by pathology. Given the rarity of the disease, there are only a few studies outlining its optimal management, nevertheless, diagnosis and treatment of this pathology can be approached by customary means, bearing extremely favorable prognosis.