Case Report
Copyright ©The Author(s) 2020.
World J Gastroenterol. Sep 28, 2020; 26(36): 5520-5526
Published online Sep 28, 2020. doi: 10.3748/wjg.v26.i36.5520
Table 1 Summary of SMARCB1 deficient pancreatic undifferentiated rhabdoid carcinoma cases in the literature along with our case
Ref.Age/genderSize/pancreatic locationHistologyTreatmentMetastasisOutcomeKRAS mutationSMARCB1 (IHC)
Agaimy et al[2]76/M5 cm/headRhabdoidSurgeryNSDOD in 1 moWild typeComplete loss
Agaimy et al[2]44/F6 cm/headRhabdoid, angiosarcoma-likeSurgeryNSNSPositive (pGly12Asp)Complete loss
Agaimy et al[2]72/M4 cm/headRhabdoid, pseudopapillary acantholytic gland-like spacesSurgeryLiver, lymph nodesDOD post-operativelyWild typeComplete loss
Agaimy et al[2]61/M5 cm/tailRhabdoid, prominent neutrophils and focal glandular formationSurgeryIntra-abdominal, stomachNSWild typeComplete loss
Sano et al[3]68/F10 cm/body, tailRhabdoidPalliativeLiver, kidneys, lungs, right adrenal gland, omentum, peritoneumDOD in 2 wkNSComplete loss
Ohike et al[4]35/F6 cm/headRhabdoid, solid/diffuseChemoLiverDOD in 7 moWild typeComplete loss
Tahara et al[5]67/F1.9 cm/bodyRhabdoid, solid/diffuseChemoLiver, lung, bone, tongue, right thighDOD in half yearWild typeComplete loss
Lehrke et al[6]NSNSRhabdoidNSNSNSNSComplete loss
Our case59/F3.1 cm/headRhabdoid, solid pseudopapillary-likeSurgeryLiverDOD in 7 moWild typeComplete loss