Case Report
Copyright ©The Author(s) 2015.
World J Gastroenterol. May 7, 2015; 21(17): 5432-5441
Published online May 7, 2015. doi: 10.3748/wjg.v21.i17.5432
Table 1 The year reported, location, size, age, sex, clinical symptoms, and imaging findings of 33 cases of hepatic perivascular epithelioid cell tumor
Year reportedReferenceAuthorsAge (yr)SexSize (cm)LocationClinical symptomsDetail of imaging findingsCountryVessels in lesion
2014our case58M4.5Lateral segmentabdominal bloatingHCC patternAsianYes
2014[6]Bergamo et al31F10.0Right lobevomiting and gastric refluxearly enhancement onlyAsian
2014[7]Zhang et al63F3.5S5NoneHCC patternEuropean
2013[8]Khaja et al51F4.0S4NoneHCC patternOther
2013[9]Tay et al51F9.0S2/3appetite lossHCC patternAsianYes
2013[10]Liu et al25F5.5S7Noneearly enhancement onlyAsian
2013[11]Shen et al55M1.5S6NoneHCC patternAsian
2013[12]Jafari et al53F7.5Lateral segmentepigastralgiaHCC patternEuropean
2013[13]Cheung et al53F10.0Right lobeabdominal discomfortHCC patternAsian
2013[14]Zhao et al58M7.6S6abdominal distentionHCC patternAsian
2013[15]Yu et al41F2.2S6abdominal pain and vomitingHCC patternAsian
2012[16]Tan et al38F4.0Right lobe(S8)3 patients; colic pain or abdominal discomfortHCC patternAsian
201234F4.3Right lobe(S8)NoneAsian
201249F2.5Left lobeNoneAsian
201275F8.0Right lobeNoneAsian
201233F2.5Right lobeNoneAsian
201271MNoneRight lobeNoneAsian
201241FmultipleLeft lobenon early enhancement-gradual enhancementAsian
2012[17]Durczyński, et al18F15.0Left lobeUnknownNoneEuropean
2011[18]Ahn et al36F7.0Left lobe(tumor palpable)HCC patternAsian
2009[19]Akitake et al36F3.5S2NoneHCC patternAsian
2009[20]Strzelczyk et al57F20.0Right lobeabdominal pain and vomitingnon-contrast CTEuropean
2009[21]Sánchez Pérez et al32F5.5S7Noneno early enhancementEuropean
2009[22]Priola et al36F11.0Left lobeabdominal painhemorrhageEuropean
2009[23]Patra et al50F15.0Right lobeabdominal painearly-gradual enhancementAsian
2008[24]Della Vigna et al46F3.5S3NoneHCC patternEuropean
2008[25]Paiva et al51F0.8Left lobeNoneNoneOther
2008[26]Zimmermann et al53M8.6Right lobeabdominal painNoneOther
2007[27]Larbcharoensub et al31F1.8S8abdominal painHCC patternAsian
2007[28]Fang et al56F5.1S4abdominal distentionenhancement in the portal phaseAsian
200763F8.0S1NoneHCC pattern and late enhancementAsian
2007[29]Svajdler et al55F3.5S4NoneHCC patternEuropean
2006[30]Parfitt et al60F14.0Right lobeabdominal discomfort and painNoneOther
Table 2 The year reported, location, size, age, sex, clinical symptoms, enhanced images and vessels within the lesions of 40 cases with hepatic epithelioid angiomyolipoma
Year reportedReferenceAuthorsAge (yr)SexSize (cm)LocationClinical symptomsDetail of imaging findingsVessels in lesionCountry
2013[31]Occhionorelli et al25F8.0Left lobeAbdominal painEarly-gradual EnhancementEuropean
2013[32]Saito et al46M1.2S2NoneEarly-gradual EnhancementAsian
2013[33]Zhao et al54F0.6S4NoneHCC patternAsian
30F3.7S7NoneNon early enhancement-gradual EnhancementAsian
49N9.7S4NoneEarly-gradual EnhancementAsian
51F3.0S5NoneHCC patternAsian
52M3.2S6NoneHCC pattern and late EnhancementAsian
2013[34]Lo et al70F24Right lobeAbdominal distentionNoneAsian
47F0.2Right lobeNoneEarly-gradual EnhancementAsian
41F10.0Left lobeAbdominal discomfortHCC patternAsian
40F9.0Right lobeEpigastralgiaHCC patternAsian
36F7.5Right lobeNoneHCC patternAsian
2012[35]Agaimy et al63F1.0S2/3NauseaHCC patternEuropean
2013[36]Ji et al64F5.0S1NoneHCC patternYesAsian
43F6.0S2/3NoneEarly-gradual EnhancementYesAsian
56F4.0S4NoneEarly-gradual EnhancementAsian
40F8.5S2/3NoneHCC patternYesAsian
46F4.2S7/8NoneHCC patternYesAsian
32F6.0S2/3NoneHCC patternYesAsian
2012[37]Xie et al32F3.4S7DyspneaHCC patternOther
2010[38]Wen et al25M4.1S4NoneHCC patternAsian
2009[39]Leenman et al29F5.0S3Abdominal painNoneOther
2009[40]Xu et al51F6.5/4S6/7, S4UnknownNo early enhancementYesAsian
42F3.2S1UnknownNo early enhancementAsian
35F6.5S6UnknownEarly enhancement onlyYesAsian
36F0.5S4UnknownEarly enhancement onlyYesAsian
17F9.0S578UnknownEarly enhancement onlyYesAsian
55F4.0S2/3UnknownEarly enhancement onlyYesAsian
36F2.0S4UnknownEarly enhancement onlyYesAsian
46F3.0S2/3UnknownEarly enhancement onlyYesAsian
47F1.5S6UnknownEarly enhancement onlyYesAsian
2009[41]Alatassi et al26F11 (multiple)MultipleNoneNoneOther
2007[42]Khalbuss et al39F12.0S2/3Abdominal painNoneOther
2006[43]Rouquie et al67F7.0S4NoneEarly enhancement onlyYesEuropean
2004[44]Tryggvason et al42F6.0S2/3Abdominal painHCC patternEuropean
2000[45]Savastano et al39F1.2S2/3UnknownHCC patternYesEuropean
2000[46]Flemming et al46F3.5/1S6, S3UnknownEarly enhancement onlyEuropean
50F6.0S1UnknownHCC patternEuropean
46F19.0S4-8UnknownHCC patternEuropean
2000[47]Yamasaki et al30F2.0Right lobeNoneEarly enhancement onlyAsian