Published online Jul 14, 2021. doi: 10.3748/wjg.v27.i26.4172
Peer-review started: January 30, 2021.
First decision: March 6, 2021
Revised: March 23, 2021
Accepted: June 22, 2021
Article in press: June 22, 2021
Published online: July 14, 2021
Core Tip: Adult pancreatoblastomas are extremely rare tumours of the pancreas. They are composed of neoplastic cells with multiple lines of differentiation and characteristic squamoid nests. They mimic other neoplasms of the pancreas, which may give rise to diagnostic difficulties. This article provides an up-to-date review of the clinical and pathologic features of pancreatoblastoma in adults, including differential diagnosis, treatment, and follow-up.