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Copyright ©The Author(s) 2021.
World J Hepatol. Nov 27, 2021; 13(11): 1727-1742
Published online Nov 27, 2021. doi: 10.4254/wjh.v13.i11.1727
Table 6 Liver transplantation in cystic fibrosis liver disease - data from few published series
Ref.
Type
Number of pediatric recipients
Type of transplants
Males
Mean age at isolated liver transplantation (yr)
Lung function after Liver transplantation
5-year survival
Milkiewicz et al[45], 2002Single center9Liver; Liver- lung -heartNot available15ImprovedNot available
Fridell et al[21], 2003Single center12Liver 83%10 ± 4.5 Improved or remained unchanged75%
Molmenti et al[47], 2003Single center10Liver90%9.7 (1.23–19)Not available60%
Mendizabal et al[44], 2011Analysis of United Network for Organ Sharing database148Liver; Liver- lung (3.4%)62%11 ± 4.7 Not available86%
Miguel et al[48], 2011Single center11Liver67%12 (5.4–17)Worsened or remained unchanged> 85%
Dowman et al[49], 2012Single center19LiverNot available11.8 (9.5–16.5)Stable/improved initially, deteriorated > 5 years after transplant> 60%