Huge primitive neuroectodermal tumor of the pancreas: Report of a case and review of the literature

Table 1 Overview of reported cases of pancreatic PNET

Reference	Age (yr)	Gender	Tumor origin	Tumor size (cm)	Therapy	Survival (cause)
Lüttges et al[5] 1997	13	Female	Pancreatic body/tail	22 × 8 × 10	Resection, chemotherapy	NR
	31	Male	Pancreatic body	-	Chemotherapy, resection	NR
Bulchmann et al[3] 2000	6	Female	Pancreatic head	4.0 × 5.4 × 3.0	Whipple resection with colon segmentectomy	6 mo (RD)
Movahedi-Lankarani et al[2] 2002	6-25 (mean 18)	4 male, 3 female	Pancreatic head	3.5 to 9.0	Whipple resection in 4 cases (2 VDC), biopsy in 3 cases (1 VDC)	Up to 48 mo
Perek et al[6] 2003	31	Male	Pancreatic head and body	10 × 12	1 Whipple resection (radiochemotheray denied), 2 Local resection + chemotherapy, 3 Resection of lung metastasis + chemotherapy	50 mo (RD)
Present case	33	Male	Pancreatic body	18 × 18 × 16	Resection, 6 cycles VIDE, VAI, AST	Alive at 1 year after diagnosis

AST: Autologous stem cell transplantation; mo: Months; NR: Not reported; RD: Recurrent disease; VDC: Vincristin, doxorubicin, cyclophosphamide; VIDE: Vincristin, ifosfamide, doxorubicin and etoposide; VAI: Vincristin, actinomycin D: Ifosfamide.