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Copyright ©2014 Baishideng Publishing Group Co.
World J Gastrointest Pathophysiol. Feb 15, 2014; 5(1): 11-17
Published online Feb 15, 2014. doi: 10.4291/wjgp.v5.i1.11
Table 1 Epidemiological, laboratory, pathological and clinical characteristics of type 1 and type 2 autoimmune pancreatitis
Type 1 AIPType 2 AIP
AgeAdultChild and adult
GenderUsually maleEqual
Serum IgG4 levelsElevatedNormal
HistologyLymphoplasmacytic sclerosing pancreatitisIdiopathic duct-centric pancreatitis
IgG4 plasma cellsWell representedRare
Granulocytic epithelial lesionsAbsentPresent
Relapse rateHighLow
Extra-pancreatic lesionsIgG4-related disease: hypophysitis, pachymeningitis, perineural mass, chronic sclerosing dacryoadenitis, chronic sclerosing sialadenitis, lymphadenopathy, thyroiditis or hypothyroidism, pseudolymphoma, breast inflammatory pseudotumor or mastitis, pulmonary inflammatory pseudotumor, nodular pleuritis, chronic gastritis, Vater’s ampulla pseudotumor, sclerosing cholangitis, lymphoplasmacytic sclerosing cholecystitis, hepatic inflammatory pseudotumor, autoimmune hepatitis, retroperitoneal fibrosis, periaortitis/periarteritis, inflammatory aneurysm, tubulointerstitial nephritisInflammatory bowel disease