Octreotide in Hennekam syndrome-associated intestinal lymphangiectasia

Table 1 Cases of intestinal lymphangiectasia treated with octreotide in the literature

Number of patients	Age of patients	Etiology of PLE	Dose of octreotide	Pre octreotide serum albumin	Post octreotide serum albumin	Ref.
6	0-24 mo	PIL	15-20 μg/kg twice daily	14-25 g/L	Normal in 3/6	[2]
1	38 yr	IL	100 μg twice daily	12 g/L	Above 40 g/L	[17]
1	21 yr	PIL	150 μg twice daily	22 g/L	39 g/L	[18]
1	25 yr	IL	Slow release octreotide 20 mg every 4 wk	20 g/L	35 g/L	[19]
1	27 yr	Type I IL	200 μg twice daily then SR octreotide 30 mg every 4 wk	19 g/L	NA (graph indicates 30-40 g/L)	[20]
1	47 yr	Cirrhosis induced IL	0.1 mg three times daily	22 g/L	28 g/L	[21]
1	17 yr	PIL	200 μg twice daily	15 g/L	22-26 g/L	[24]
2	2-12 mo	HS associated IL	100 μg twice daily	16 g/L	28-36 g/L	Current report

IL: Intestinal lymphangiectasia; PLE: Protein losing enteropathy; PIL: Primary intestinal lymphangiectasia; SR: Slow release; NA: Not available; HS: Hennekam syndrome.