Combined hepatic resection with fenestration for highly symptomatic polycystic liver disease: A report on seven patients

Table 1 Clinical findings of patients with PLD

Patient no.	Age (yr)	Gender	Family history	Symptoms	Other involved organs	Previous treatment
1	48	Female	No siblings	Abdominal distention, regurgitation	None	None
2	41	Female	Father, two sisters, brother	Abdominal pain and distention	Kidney	PCA + AS (5 times)
3	54	Female	Sister	Early satiety, regurgitation	Kidney	PCA + AS (2 times)
4	45	Male	Sister	Abdominal pain and distention	Kidney	PCA + AS (2 times)
5	43	Female	Sister, brother, grandmother	Abdominal pain and distention, early satiety, dyspnea	Kidney	PCA + AS (2 times)
6	36	Female	Mother, sister	Abdominal pain and distention, early satiety, supine dyspnea	Kidney	None
7	42	Female	Father	Abdominal distention, regurgitation	Kidney	None

PCA + AS, Percutaneous cyst aspiration with alcohol sclerotherapy.

Table 2 Operative data, surgical outcome, and follow-up of patients with PLD

Patient no.	Hepatic resection	Blood loss (mL)	Cystic fluid aspirated (mL)	Days of hospital stay (after operation)	Postoperative complications	Symptomatic relief	Reduction in size of liver
1	III, IVb, V	400	1500	21 (12)	Acites	Marked	Marked
2	II, III, V	800	3000	25 (14)	Acites	Marked	Marked
3	Right semi hepatectomy, cholecystectomy	200	1200	16 (8)	Mild acites	Marked	Marked
4	Right smi hepatectomy, cholecystectomy	300	1800	24 (16)	Moderate acites	Marked	Marked
5	II, III, IVb	1500	6500	83 (29)	Severe acites,left pleural effusion	Moderate	Moderate
6	II, III, VI, VII	3400	4000	42 (16)	Severe acites, right pleural effusion	Marked	Marked
7	II, III, VI	300	2500	27 (11)	Acites	Marked	Marked

Table 3 Review of the literature: mortality, morbidity and outcome of patients with PLD treated by combined hepatic resection an cystic fenestration

Authors	No. of patients	Mortality (no.)	Morbidity (no.)	Follow-up (mos)	No. of symptom- free patients
Armitage et al[12] (1984)	1	0	0	12	1
Iwatsuki et al[13] (1988)	6	0	0	-	-
Newman et al[2] (1990)	9	1	6	17	7
Sanchez et al[8] (1991)	2	0	0	48	2
Vauthey et al[1] (1992)	5	0	4	14	5
Henne-Bruns et al[14] (1993)	8	0	3	15	6
Soravia et al[15] (1995)	10	1	2	68	6
Que et al[16] (1995)	31	1	18	29	28
Vons et al[17] (1998)	12	1	10	34	1 0
Johnson et al[18] (1999)	1	0	0	18	1
Our series	7	0	7	0	6
Total	92	4 (4.3%)	50 (54.3%)		72 (78.3%)