Case Report
Copyright ©The Author(s) 2022. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. May 16, 2022; 10(14): 4519-4527
Published online May 16, 2022. doi: 10.12998/wjcc.v10.i14.4519
Plexiform neurofibroma of the cauda equina with follow-up of 10 years: A case report
Zilvinas Chomanskis, Raimondas Juskys, Saulius Cepkus, Justyna Dulko, Vaiva Hendrixson, Osvaldas Ruksenas, Saulius Rocka
Zilvinas Chomanskis, Saulius Rocka, Department of Neurology and Neurosurgery, Institute of Clinical Medicine, Faculty of Medicine, Vilnius University, Vilnius 03104, Lithuania
Raimondas Juskys, Anatomy, Histology and Anthropology Department, Vilnius University, Faculty of Medicine, Vilnius 03104, Lithuania
Saulius Cepkus, Department of Neurosurgery, Republican Vilnius University Hospital, Vilnius 04130, Lithuania
Justyna Dulko, Faculty of Medicine, Vilnius University, Vilnius 03104, Lithuania
Vaiva Hendrixson, Institute of Biomedicine, Faculty of Medicine, Vilnius University, Vilnius 03104, Lithuania
Osvaldas Ruksenas, Institute of Biosciences, Life Sciences Centre, Vilnius University, Vilnius 10257, Lithuania
Author contributions: Chomanskis Z, Cepkus S and Rocka S were the patient’s neurosurgeons, reviewed the literature and contributed to manuscript drafting; Chomanskis Z followed the patient; Juskys R and Dulko J reviewed the literature, contributed to manuscript drafting and edition; Hendrixson V, Ruksenas O, Chomanskis Z were responsible for the revision of the manuscript for important intellectual content; all authors issued final approval for the version to be submitted.
Informed consent statement: Informed written consent was obtained from the patient for publication of this report and any accompanying images.
Conflict-of-interest statement: The authors declare that they have no conflict of interest.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Raimondas Juskys, MD, Assistant, Anatomy, Histology and Anthropology Department, Vilnius University, Faculty of Medicine, Ciurlionio str. 21, Vilnius 03104, Lithuania. raimondas.juskys@mf.vu.lt
Received: August 2, 2021
Peer-review started: August 2, 2021
First decision: September 28, 2021
Revised: October 9, 2021
Accepted: March 25, 2022
Article in press: March 25, 2022
Published online: May 16, 2022
Core Tip

Core Tip: Plexiform neurofibroma manifestation in the region of cauda equina is an exceptionally rare event, as only 7 cases were described in the literature up-to-date. We present the 8th such case with the follow-up period of 10 years. Diagnosis was delayed because patient was initially misdiagnosed with the idiopathic polyneuropathy. In order to minimize the necessity for additional interventions in the future, we would recommend to pursue an extensive decompression with duraplasty and primary spinal fixation as the initial management of choice. However, we would strongly suggest to abstain from tumor resection attempts as risk of neurological complications is high.