Biliary atresia and congenital disorders of the extrahepatic bile ducts

Table 1 Associated anomalies of embryonic or syndromic biliary atresia

Origin of anomaly	Description
Splenic anomalies	Asplenia, double splen, polysplenia
Cardiovascular anomalies	Interrupted/absent inferior vena cava, dextrocardia, left atrial isomerism, other cardiac anomalies (pulmonary stenosis, ASD, VSD, PDA, total anomalous pulmonary venous return, coarctation of the aorta, TOF, hypoplastic left heart syndrome)
Portal vein and hepatic artery anomalies	Preduodenal portal vein, anomaly originated hepatic artery
Abdominal anomalies	Situs inversus, midgut malrotation, intestinal atresia (esophageal, duodenal or jejunal), anular pancreas, short pancreas
Renal anomalies	Renal agenesis, hypoplastic or polycystic kidneys
Other uncommon anomalies	Primary ciliary dyskinesia, caudal regression syndrome

ASD: Atrial septal defect; PDA: Patent ductus arteriosus; TOF: Tetralogy of Fallot; VSD: Ventricular septal defect.