Case Report
Copyright ©2014 Baishideng Publishing Group Inc.
World J Gastroenterol. Sep 21, 2014; 20(35): 12662-12667
Published online Sep 21, 2014. doi: 10.3748/wjg.v20.i35.12662
Table 1 Review of literature
AuthorYear of publicationPatients (n)SexAge(in year)Clinical presentationLiver enzymesOutcome
Chattopadhyay et al[15]20111Female20Fever, polyarthritis, jaundiceElevatedRemission
Choi et al[16]20081FemaleUnknownButterfly-type facial erythemaElevatedRemission
Chowdhary et al[8]20086UnknownUnknownUnknownUnknownUnknown
Deen et al[17]200943 female 1 maleMedian 11 Range 11-13Jaundice, splenomegaly, cutaneous involvement, articular involvement, proteinuria (> 0.5 g/d), cardiopulmonary involvementElevatedRemission in all cases
Efe et al[18]20114FemaleMedian 35UnknownElevatedUnknown
Range 27-40
Iwai et al[19]20031Female60Elevated liver enzymesElevatedRemission
Kaw et al[20]20061Female34Arthralgia, myalgias, skin rash, nauseaElevatedRemission
Kooy et al[21]19961UnknownUnknownUnknownElevatedRemission
Koshy et al[22]20121Female30Jaundice, abdominal distentionElevatedExitus letalis1
Mackay et al[11]19991Female16Failure to thrive, jaundice, non-erosive arthritis, oral aftous lesionsElevatedProgress
Moriwaki et al[23]19871UnknownUnknownUnknownUnknownUnknown
Satoh et al[24]19972UnknownUnknownUnknownUnknownRemission
Suzuki et al[25]19931Female33Intermittend fever, polyarthralgia, cutaneous involvement, pericardial effusionElevatedRemission
Takahashi et al[26]20071Female69Fever, cough, pleural and pericardial effusionElevatedRemission
Tojo et al[27]20045FemaleMedian 43Raynaud’s phenomenon, arthralgia, butterfly-type facial erythema, dry mouth, jaundice, edema, ascites, pleural effusion, struma, skin ulcer, fatigue, feverElevated in 4 of 5 casesRemission in all cases
Range 21-56
Usta et al[28]20071Female12Jaundice, hepatosplenomegaly, polyarthralgia, malaise, butterfly-type facial erythema, arthritisElevatedStable
Yamasaki et al[29]20041Female48AscitesElevatedRemission
Yoon et al[30]20032FemaleUnknownUnknownElevatedUnknown