Editorial
Copyright ©2011 Baishideng Publishing Group Co.
World J Gastroenterol. Dec 7, 2011; 17(45): 4937-4944
Published online Dec 7, 2011. doi: 10.3748/wjg.v17.i45.4937
Table 2 Phenotypes of mouse models of enteric nervous system defects
Wild-typeColonic aganglionosisTotal intestinal aganglionosisHypoganglionosis
Ret+/-51/51-/-C620R/+
9/9S697A/S697AY1062F/Y1062F
Y162F/+C620R/C620R
Ednbsl/+sl/sl
Ednrbtm1Ywa/Ednrbtm1Ywa
Et3ls/+ls/ls
Et3tm1Ywa/ Et3tm1Ywa
Sox10Dom/+ (~80%)Dom/+ (~20%)Dom/Dom
LacZ/+ (~80%)LacZ/+ (~20%)LacZ/LacZ
InteractionsRet+/-; Ednrbs/sRet51/51; Et3ls/ls
Ret51/+; Et3ls/lsSox10Dom/+; Et3ls/ls
Sox10Dom/+; Edrnbsl/sl
Other genotypesSall4-/-Gdnf-/-Gdnf+/-
B1Intergrin-/-Gfra1-/-Hlx1-/-
Ece1-/-Phox2b-/-
Pax3-/-