Postpartum hemophagocytic lymphohistiocytosis: A case report

Table 2 Number of diagnostic criteria met, treatments, and outcomes

Case No	Diagnostic criteria met	Primary therapy	Outcome
1	1,2,3,4,5,7,8	HLH-04	Died
2	1,2,3,4,5,6,7	HLH-04	Survived
3	1,3,4,5,7,8	HLH-04	Survived
4	1,2,4,5,6,7,8	HLH-94	Survived
5	1,2,4,5,6,7,8	HLH-94	Survived
6	1,3,4,5,7	HLH-94	Died
7	1,2,4,6,7,8	FD	Survived
8	1,2,4,5,6,7,8	DEP	Survived
9	1,2,3,4,5,6,7,8	HLH-94 with anakinra	Survived
10	1,2,3,4,5,7	HLH-04	Survived
11	1,2,3,4,7	Methylprednisolone	Survived

Diagnostic criteria met, 1: Fever; 2: Splenomegaly; 3: Cytopenia affecting ≥ 2 of 3; 4: Hypertriglyceridemia and/or hypofibrinogenemia; 5: Hemophagocytosis in bone marrow or spleen or lymph nodes or liver; 6: Low or absent natural killer cell activity; 7: Ferritin elevation; 8: Elevated soluble cluster of differentiation 25. DEP: Doxorubicin + etoposide + methylprednisolone; FD: Fludarabine + prednisolone; HLH: Hemophagocytic lymphohistiocytosis.