Conservative management of small bowel perforation in Ehlers-Danlos syndrome type IV

Table 2 Vascular Ehlers-Danlos syndrome: Villefranche diagnostic criteria

Major diagnostic criteria	Minor diagnostic criteria
Arterial, digestive or uterine fragility or rupture	Positive family history
Thin, translucent skin	Sudden death in a close relative
Extensive bruising	Acrogeria
Characteristic facial appearance	Hypermobility of small joints
	Tendon and muscle rupture
	Talipes equinovarus (clubfoot)
	Early onset varicose veins
	Spontaneous pneumo or hemothorax

It’s adapted from Germain et al[5] and Beighton et al[6].